O diagnóstico diferencial inclui cistos broncogênicos ou entéricos, sequestração pulmonar, enfisema lobar congênito e massas mediastinais.(41) A radiografia. Request PDF on ResearchGate | Enfisema lobar congénito: Presentación de 4 casos | SUMMARY Congenital lobar emphysema is an unfrequent congenital. Congenital lobar overinflation (CLO), previously called congenital lobar emphysema, is a congenital lung abnormality that results in progressive overinflation of.

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All patients were treated with lobectomy.

Diagnostic methods Chest X ray and CT scan are the key imaging modalities used for diagnosis. The ex utero intrapartum therapy procedure for high-risk fetal lung lesions.

Related articles Unilateral hypertranslucent hemithorax. Echocardiography to detect concomitant heart disease can also be performed. Chest X encisema shows hyperlucent affected lobes with mediastinal shift and collapse of ipsilateral unaffected enfisema lobar congenito.


Most cases are idiopathic. Most cases are idiopathic. What happens to the pulmonary vasculature in enfisema lobar congenito affected lobe? Case 4 Case 4. Child is asymptomatic in long term follow up.

We use cookies to help provide and enhance our service and tailor content and ads. Hemoptysis from an unusual pulmonary arteriovenous malformation.


Previous Article Vol Video-assisted thoracoscopic surgical excision of cystic lung disease in children. Case 1 Case 1.

Orphanet: Enfisema lobar congenito

Diagnostic methods Chest X ray and CT scan are the enfisema lobar congenito imaging modalities used for diagnosis. Key-words Congenital lobar emphysema. Elsevier About ScienceDirect Remote access Shopping cart Contact and support Terms and conditions Privacy policy We use cookies to help provide and enhance our service and tailor content and ads. Services on Demand Journal. Lobectomy has better results than clinical treatment and should be chosen.

Congenital lobar hyperinflation Infantile lobar hyperinflation Prevalence: CT scan provides details of affected lobes and vascular involvement. Check if you have access through your login credentials or your institution.

The morphologic spectrum of infantile lobar emphysema: Synonyms or Alternate Spellings: In the immediate postnatal period the affected lobe tends to appear enfisema lobar congenito and homogeneous because of fetal lung fluid or it may show a diffuse reticular pattern that represents distended lymphatic channels filled with fetal lung fluid. Cystic adenomatoid malformation of the lung presenting in adulthood.

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Congenital cystic adenomatoid malformation of the lung. The chest x-ray at admission was suggestive of CLE and the diagnosis was confirmed by computorized tomography. There are many presumed mechanisms for progressive overdistension of a lobe including obstruction, cartilage deficiency, dysplasia, and immaturity 2.

How to cite this article. Recommended articles Citing articles 0. About Blog Go ad-free. Asymptomatic or mildly symptomatic cases can be managed conservatively but follow up is necessary.

Case 2 Case 2. Only comments written in English can be processed.

Congenital Lobar Emphysema CLE is a rare malformation of lung development, which may be the cause of respiratory insufficiency in the suckling child.

Video-assisted thoracoscopic surgery for intralobar pulmonary sequestration. Fetal cystic lung lesions: A lobectomy can be considered in severe cases 3.


Thorax, 14pp. Pediatrics, 34pp. Cystic lung lesions in the pediatric and adult population: To quiz yourself on this article, log in to see multiple choice questions.